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Excessive dietary lipid intake provokes an acquired form of lysosomal lipid storage disease in the kidney

Rampanelli, Elena ; Ochodnicky, Peter ; Vissers, Johannes P. C. ; Butter, Loes M. ; Claessen, Nike ; Calcagni, Alessia ; Kors, Lotte ; Gethings, Lee A. ; Bakker, Stephan J. L. ; de Borst, Martin H. ; Navis, Gerjan J. ; Liebisch, Gerhard ; Speijer, Dave ; van den Bergh Weerman, Marius A. ; Jung, Bettina ; Aten, Jan ; Steenbergen, Eric ; Schmitz, Gerd ; Ballabio, Andrea ; Florquin, Sandrine ; Aerts, Johannes M. F. G. ; Leemans, Jaklien C.



Zusammenfassung

Obesity and dyslipidaemia are features of the metabolic syndrome and risk factors for chronic kidney disease. The cellular mechanisms connecting metabolic syndrome with chronic kidney disease onset and progression remain largely unclear. We show that proximal tubular epithelium is a target site for lipid deposition upon overnutrition with a cholesterol-rich Western-type diet. Affected proximal ...

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