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Nachtigal, Anna-Lena ; Milenkovic, Andrea ; Brandl, Caroline ; Schulz, Heidi L. ; Duerr, Lisa M. J. ; Lang, Gabriele E. ; Reiff, Charlotte ; Herrmann, Philipp ; Kellner, Ulrich ; Weber, Bernhard H. F.

Mutation-Dependent Pathomechanisms Determine the Phenotype in the Bestrophinopathies

Nachtigal, Anna-Lena, Milenkovic, Andrea, Brandl, Caroline , Schulz, Heidi L., Duerr, Lisa M. J., Lang, Gabriele E., Reiff, Charlotte, Herrmann, Philipp, Kellner, Ulrich and Weber, Bernhard H. F. (2020) Mutation-Dependent Pathomechanisms Determine the Phenotype in the Bestrophinopathies. International Journal of Molecular Sciences 21 (5), p. 1597.

Date of publication of this fulltext: 11 Oct 2021 13:01
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Item typeArticle
Journal or Publication TitleInternational Journal of Molecular Sciences
Publisher:MDPI
Place of Publication:BASEL
Volume:21
Number of Issue or Book Chapter:5
Page Range:p. 1597
Date2020
InstitutionsMedicine > Lehrstuhl für Augenheilkunde
Medicine > Lehrstuhl für Humangenetik
Medicine > Institut für Epidemiologie und Präventivmedizin > Lehrstuhl für Genetische Epidemiologie
Identification Number
ValueType
10.3390/ijms21051597DOI
KeywordsRETINAL-PIGMENT EPITHELIUM; PLURIPOTENT STEM-CELLS; BEST-DISEASE; MISSENSE MUTATIONS; ACIDIC PH; RPE CELLS; GENE; DEGRADATION; PROTEIN; VMD2; bestrophin-1; BEST1; induced pluripotent stem cell; retinal pigment epithelium; ER-associated degradation; endo-lysosomal degradation pathway; pathomechanism; Best vitelliform macular dystrophy; Best disease; autosomal recessive bestrophinopathy; autosomal dominant vitreoretinochoroidopathy
Dewey Decimal Classification600 Technology > 610 Medical sciences Medicine
StatusPublished
RefereedYes, this version has been refereed
Created at the University of RegensburgYes
Item ID50249

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