Zusammenfassung
We report the case of an unusually severe bleeding episode following adenotomy in an infant. Preoperative laboratory coagulation tests (aPTT, PT) were normal. We diagnosed type-1 von Willebrand disease (VWD) on the basis of abnormal history of the patient and her family and low von Willebrand factor values. The multimeric pattern was normal. We also give a summary of the current classification, diagnosis and therapy of VWD.